PPB occurs most often in children younger than four with most cases diagnosed between 3 to 4 years, sometimes in children ages four to eight, and very rarely in older children, teenagers, and adults. PPB occurs about equally in boys and girls.

PPB is rare. Only 10 to 20 people are diagnosed with PPB each year in the United States.

The overall survival rate (percentage of people who survive after the tumor is detected, excluding those who die from other diseases) of people with PPB is hard to estimate, given the rare nature of this disease. Talk with your doctor about your prognosis and what individual factors this is based on.

Survival statistics should be interpreted with caution. It is not possible to tell a person how long he or she will live with PPB. Survival statistics may not represent advances made in the treatment or diagnosis of PPB. Learn more about understanding statistics [2].

Sources: International PPB Registry