Pleuropulmonary Blastoma - Childhood: Statistics

Approved by the Cancer.Net Editorial Board, 01/2020

ON THIS PAGE: You will find information about the number of children who are diagnosed with PPB each year. You will also read general information on surviving the disease. Remember, survival rates depend on several factors. Use the menu to see other pages.

PPB is rare. PPB occurs most often in children younger than 12, with most children diagnosed between the ages of 3 to 4. PPB is rarely diagnosed in teenagers and adults. PPB occurs about equally in boys and girls.

The overall survival rate tells you what percent of children live a certain amount of time after the cancer is found. Percent means how many out of 100. The overall survival rate for children with PPB is hard to estimate because the disease is rare. It is estimated that about 89% of people with Type I PPB are successfully treated, while about 50% to 70% of those with Type II or Type III are. Type I PPB can recur, or come back, as Type II or III PPB. Talk with your doctor about your child’s prognosis and what individual factors it is based on.

It is important to remember that statistics on the survival rates for children with PPB are an estimate. The estimate comes from data based on the number of children with this cancer in the United States. Estimates may not represent advances made in the treatment or diagnosis of PPB. Talk with your child’s doctor if you have any questions about this information. Learn more about understanding statistics.

Statistics adapted from the International Pleuropulmonary Blastoma/DICER1 Registry and the National Organization for Rare Disorders (all accessed January 2020).

The next section in this guide is Risk FactorsIt explains what factors may increase the chance of developing PPB. Use the menu to choose a different section to read in this guide.